Proteins › Globular Proteins

Hemoglobin Allosteric Effects

Notes

Hemoglobin Allosteric Effects

Sections


Overview

Definitions

Bohr effect

  • Low pH enhances hemoglobin oxygen dissociation

2, 3 Bisphosphoglycerate (BPG)

  • Molecule localized in red blood cells
  • Decreases hemoglobin's oxygen affinity

Dissociation curve

  • % oxygen saturation vs. oxygen partial pressure (torr)
  • Cooperative binding produces sigmoidal binding curve

Bohr Effect

  • Decrease in blood pH shifts curve to the right
  • Hemoglobin requires greater pO2 in peripheral tissues to reach 50% saturation
  • Lowering pH decreases hemoglobin's oxygen affinity

2,3 BPG

  • Hemoglobin without 2,3 BPG: shifts curve to the left (hyperbolic like myoglobin)
  • Adding 2,3 BPG: shifts curve back to the right.

BOHR EFFECT

Beta subunit

  • Aspartate (-) and histidine (+)

T-form: histidine pKa = 8.0 (side chains close to each other)

  • T-form favored when blood pH --> has a high affinity for H+

R-form: histidine pKa drops to 7.1 (side chains move apart)

  • Histidine loses H+
  • R-form favored when blood pH is high and H+ concentration is low

Carbon dioxide

  • CO2 + H2O --> H2CO3 (carbonic acid) --> HCO3- (bicarbonate) + H+ (reversible)
  • Carbonic anhydrase catalyzes carbonic acid formation
  • Carbonic acid spontaneously loses proton to form bicarbonate
  • Bicarbonate = blood buffer
  • Increase in CO2 --> lowers blood pH --> favors T-form hemoglobin

Carbaminohemoglobin: CO2 binds N-terminal amino acids in hemoglobin

2,3 BPG

  • Has strong negative charge: binds central cavity in hemoglobin
  • Stabilizes the T-form (only binds T-form)

CARBON MONOXIDE

  • Binds iron center with 220 times the affinity of O2 (irreversible)
  • Permanently increases oxygen affinity of remaining heme groups for oxygen
  • Decreases oxygen release in peripheral tissues

CLINICAL CORRELATION

Acetazolamide

  • Carbonic anhydrase inhibitor used to treat altitude sickness
  • Increases bicarbonate excretion by kidneys
  • Makes blood more acidic, promotes oxygen release in peripheral tissues

High altitude conditions

  • Individuals adapted to high altitude produce more 2,3 BPG
  • Favors T-form hemoglobin and O2 release: more efficient O2 delivery

Tobacco smoke

  • Smokers have elevated blood CO: hinders O2 delivery
  • Can produce tissue hypoxia

Full-Length Text

  • Here we will learn about the Bohr effect, and discuss the effects of 2,3 bisphosphoglycerate and carbon monoxide on hemoglobin.
  • To begin, start a table to list out each of the key topics we'll learn.
    • Bohr effect, which describes the effects of pH and carbon dioxide on hemoglobin binding.
    • 2,3 Bisphosphoglycerate (BPG), a molecule localized in red blood cells that decreases hemoglobin's affinity for oxygen.
    • Carbon monoxide, which increases hemoglobin's oxygen affinity and can produce toxic effects in the body.
  • As a review, draw hemoglobin's sigmoidal dissociation curve.
  • Label the x-axis partial pressure and the y-axis percent saturation.

Now, let's illustrate the first allosteric effect: the Bohr Effect.

  • Draw another sigmoidal curve to the right of the first one.
  • Show that a decrease in blood pH, shifts hemoglobin's dissociation curve to the right.
  • What does this mean?
    • Extend the horizontal line that demarcates 50% saturation.
    • Show that it intersects the second curve at a greater partial pressure of oxygen: lowering pH decreases hemoglobin's affinity for oxygen.
  • To better understand this, draw the three-dimensional structure of hemoglobin: with two alpha subunits and two beta subunits.

Let's take a closer look at a beta-subunit.

  • Within it draw two functional groups: that of aspartate (negative) and histidine (positive).
  • Indicate that in T-form hemoglobin, these side chains are close to each other, which raises the pKa of histidine to 8.0.
    • Thus, hemoglobin has a high affinity for protons in the deoxygenated state (high pKa means a high proton affinity).

Now, let's draw these groups in R-form hemoglobin.

  • Show that they are farther apart, and that the pKa of histidine drops to 7.1.
    • As we have seen, the transition between T-form and R-form hemoglobin causes shifts in amino acid conformations throughout the entire protein.
  • Show that because its pKa decreases, histidine loses a proton.
  • Thus, write that R-form is favored when blood pH is high, and the proton concentration is low.
  • Now, write that T-form is favored when the blood pH is low, and the proton concentration is high.
    • Thus, a low pH enhances oxygen dissociation and shifts hemoglobin's dissociation curve to the right.

Now, we know that a low pH enhances oxygen dissociation. But what produces low blood pH in the first place?

  • Carbon dioxide!
  • Write out the following equation:
    • Carbon dioxide plus water reversibly converts to carbonic acid.
  • Show that the enzyme carbonic anhydrase catalyzes this reaction.
  • Next, indicate that carbonic acid spontaneously loses its proton to form bicarbonate.
    • Thus bicarbonate releases protons into the blood stream.
  • Indicate that bicarbonate functions as a buffer in the blood.
  • As a clinical correlation, write that acetazolamide is a carbonic anhydrase inhibitor that is often used to treat altitude sickness.
    • How does it work? It produces an increase in bicarbonate excretion by the kidneys, via a mechanism we will not cover here.
    • As a result, it makes the blood more acidic, and promotes the release of oxygen in the peripheral tissues.
  • Finally, write that an increase in carbon dioxide in the body lowers blood pH and favors T-form hemoglobin.
    • This facilitates hemoglobin's physiologic function in the body.
  • Note that carbon dioxide can also form carbaminohemoglobin by binding to N-terminal amino acids in hemoglobin. We will not discuss this, here.

Now that we have learned the Bohr effect, let's move on to 2,3-bisphosphoglycerate (BPG), a molecule synthesized by red blood cells.

Our current sigmoidal dissociation curve already accounts for the allosteric effects of normal 2,3-BPG levels in red blood cells.

  • To visualize 2,3-BPG's effects, draw a hyperbolic curve to the left of the hemoglobin curve.
    • It should resemble myoglobin's dissociation curve.
  • Indicate that this curve represents hemoglobin without 2,3-BPG.
    • Thus, without 2,3-BPG, hemoglobin's oxygen affinity increases dramatically.
  • Show that adding 2,3-BPG shifts the curve back to the right.

How does 2,3-BPG lower hemoglobin's oxygen affinity? Let's illustrate this, now.

  • To do this, take a closer look at the center of our hemoglobin molecule: the cavity created at the intersection of all four subunits.
  • Draw histidine residues at the periphery of each of the beta subunits.
  • Show that these histidines are positively charged; they repel each other.
  • Now, importantly, label this diagram the T-form (deoxygenated hemolgobin).

Now, let's add 2,3-BPG.

  • Draw a 2,3-BPG molecule within this central cavity.
  • Indicate that it has a strong negative charge, which stabilizes the T-form.
    • Other positively charged amino acid side chains also bind 2,3 BPG here, but we won't draw all of them.
  • Now, write that 2,3-BPG only binds the T-form.
    • It encourages oxygen dissociation, and facilitates oxygen delivery!
  • As a clinical correlation, indicate that individuals that have adapted to high altitude conditions produce more BPG.
    • Why? More BPG favors T-form hemoglobin and oxygen release; it allows hemoglobin to deliver more oxygen to the peripheral tissues.

Finally, let's illustrate carbon monoxide.

  • Draw a simplified hemoglobin iron center.
  • Show that carbon monoxide irreversibly binds it.
    • We draw it at an angle because a distal histidine causes it to bend.
  • Write that carbon monoxide binds iron with an affinity 220 times greater than oxygen!
  • Indicate that by irreversibly binding iron, it permanently increases the oxygen affinity of the remaining heme groups for oxygen.
    • Thus, it pushes the hemoglobin dissociation curve to the left.

What are the physiological consequences?

  • Indicate that carbon monoxide leads to decreased oxygen release in the peripheral tissues.
  • As a clinical correlation, write that people who regularly smoke tobacco have elevated levels of carbon monoxide in their blood, which hinders hemoglobin's ability to deliver oxygen.
    • Thus, a consequence of elevated carbon monoxide is tissue hypoxia.