Q. A 3-year-old girl is brought to the pediatrician's office by her parents who are concerned about her lagging behind her peers in growth. On examination, the child has noticeable hepatomegaly and appears to be of shorter stature compared to other children her age. Laboratory findings reveal mild hypoglycemia, hyperlipidemia, and ketosis. Serum lactate levels are within the normal range. To further evaluate the hypoglycemia, a glucagon challenge is performed, which results in a subdued increase in glucose levels. Given these findings, what is the most likely diagnosis?

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