Q. A 4-month-old boy is brought to the pediatric clinic by his concerned parents due to his rapidly enlarging abdomen. His parents mention he feeds well and his development seems on track. On physical examination, you note significant hepatomegaly. No neurologic symptoms are identified and his vital signs are within the normal range. The parents mention that they had recently taken the boy to another hospital due to a suspicion of a liver issue, where abnormal liver function tests were found: AST 626 IU/L, ALT 262 IU/L, and ALP 300 IU/L. They hand you the report of a liver biopsy from that visit, which describes micronodular cirrhosis with marked intracytoplasmic glycogen deposits. Based on the clinical findings and liver biopsy report, what is the most likely diagnosis?

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